SOCIETY FOR THE STUDY
OF INBORN ERRORS OF METABOLISM

Komrower Commemorative Lectures

The Komrower Lecture is an annual award given by the SSIEM. This lecture is delivered each year at the SSIEM Symposium by someone who is considered, by the SSIEM Council, to have made a major contribution to Inborn Errors of Metabolism. The SSIEM Council is responsible for inviting the Komrower Lecturer but will seek the opinion of the Local Organising Committee for the Symposium. 

The Komrower Lecturer is introduced by the Chairperson of the SSIEM and there are no questions after the lecture. 

The Kromrower Lecture entails:
  • Invitation to present at the SSIEM Annual Symposium. The title of the presentation is entirely up to the individual
  • Certificate
  • A monetary reward of €1,000.00
  • Full registration to the Symposium including Networking Events
  • Travel Costs to the Symposium
  • Four Nights Accommodation at the Symposium Hotel

Previous Komrower Commemorative Lectures

Year   

Place

Speaker

Title

2023

Jerusalem

Prof Viktor Kožich

Molecular basis of phenotype expression in homocystinuria: where are we thirty years later?

2022

Freiburg

Prof Dr B Plecko

On pathways and blind alleys

2021

Virtual meeting  

Prof K Ounap

The identification of new rare metabolic diseases: an example of the tremendous impact on Estonia’s detection rate by new technologies

2020  

Virtual meeting 

Prof E Van Schaftingen   

Elucidating the causes of metabolic disorders: the new veins to explore

2019

Rotterdam

Dr C Vianey-Saban

From fatty acid oxidation to riboflavin Make metabolites great again

2018

Athens

Prof P T Clayton

Restoring missing metabolites: from bile to acid to B6

2016

Rome

Prof M Zeviani

Mitochondrial Disorders, a journey through the magic circle and beyond

2015

Lyon

Prof B T Poll-The

Peroxisomal disorders and more…: Why I have not stopped examining patients

2014

Innsbruck

Prof G Brown

A wide circle around lactic acid

2013

Barcelona

Dr C Dionisi-Vici

The daily challenge of understanding and treating metabolic disorders in children

2012

Birmingham

Prof R J A Wanders

Inborn errors of metabolism including peroxisomal diseases in a changing world of omics and systems biology

2011

Geneva

Dr M T Vanier

Lysosomal neurolipidoses: the enigmas and the challenges

2010

Istanbul

Prof B Wilcken

Newborn Screening: How are we travelling? Where we might get to?

2008

Lisbon

Prof N Gregersen

Mitochondrial fatty acid oxidation defects, remaining challenges

2007

Hamburg

Prof W S Sly

Evolution of therapy for lysosomal diseases

2005

Paris

Prof J Leonard

The treatment of inborn errors of metabolism

2004

Amsterdam

Prof M Gibson

Gamma-hydroxybutyric aciduria: a biochemist’s education from a heritable disorder of GABA metabolism

2002

Dublin

Prof J Jaeken

Congenital disorders of glycosylation: its all in it

2001

Prague

Prof H Galjaard

New names for old disciplines

1999

Genova

Prof J M Saudubray

Genetic hypoglycaemia

1998

York

Prof D Valle

Ornithine metabolism, metabolic network and normal biology

1997

Gothenburg

Prof S J Segal

Galactosaemia today: the enigma and the challenge

1996

Cardiff

Dr A M Spiegel

Inborn errors of signal transduction mutations in G Protein-coupled receptors as a cause of disease

1995

Toledo

Dr G Salem

Abnormal cholesterol biosynthesis in sitosterolaemia and the Smith-Lemli-Opitz syndrome

1994

Edinburgh

Prof H W Moser

Adrenoleukodystrophy, natural history, treatment and outcome

1993

Manchester

Prof J P Kraus

Molecular basis of phenotype expression in homocystinuria

Previous Noel Raine Award Winners

 

 Year   Award Winner
1981  Prof R Matalon
1982  Prof K Tada
1983  Prof S L C Woo and Dr F Guttler
1984  Prof S K Wadman 
1985  Prof R J A Wanders 
1986  Dr K M Gibson 

Komrower Commemorative Lectures

KOMROWER COMMEMORATIVE LECTURES

 

Year Place Speaker Title
2021      
2020 Virtual Meeting Prof E Van Schaftingen Elucidating the causes of metablic disorders: the new veins to explore
2019 Rotterdam Dr C Vianey-Saban

From fatty acid oxidation to riboflavin 
Make metabolites great again

2018 Athens Prof P T Clayton  Restoring missing metabolites: from bile acid to B6
2016  Rome  Prof M Zeviani  Mitochondrial Disorders, a journey through the magic circle and beyond
2015 Lyon Prof B T Poll-The Peroxisomal disorders and more…: Why I have not stopped examining patients
2014  Innsbruck Prof G Brown  A wide circle around lactic acid 
2013  Barcelona  Dr C Dionisi-Vici  The daily challenge of understanding and treating metabolic disorders in children 
2012  Birmingham  Prof R J A Wanders  Inborn errors of metabolism including peroxisomal diseases in a changing world of omics and systems biology
2011 Geneva Dr M T Vanier Lysosomal neurolipidoses: the enigmas and the challenges
2010 Istanbul Prof B Wilcken Newborn Screening: How are we travelling? Where we might get to?
2008 Lisbon Prof N Gregersen Mitochondrial fatty acid oxidation defects, remaining challenges
2007 Hamburg Prof W S Sly Evolution of therapy for lysosomal diseases
2005 Paris Prof J Leonard The treatment of inborn errors of metabolism
2004 Amsterdam Prof M Gibson Gamma-hydroxybutyric aciduria: a biochemist’s education from a heritable disorder of GABA metabolism
2002 Dublin Prof J Jaeken Congenital disorders of glycosylation: its all in it
2001 Prague Prof H Galjaard New names for old disciplines
1999 Genova Prof M Saudubray Genetic hypoglycaemia
1998 York Prof D Valle Ornithine metabolism, metabolic network and normal biology
1997 Gothenburg Prof S J Segal Galactosaemia today: the enigma and the challenge
1996 Cardiff Dr A M Spiegel Inborn errors of signal transduction mutations in G Protein-coupled receptors as a cause of disease
1995 Toledo Dr G Salem Abnormal cholesterol biosynthesis in sitosterolaemia and the Smith-Lemli-Opitz syndrome
1994 Edinburgh Prof H W Moser Adrenoleukodystrophy, natural history, treatment and outcome
 1993 Manchester  Prof J P Kraus  Molecular basis of phenotype expression in homocystinuria



Previous SSIEM Award Winners

 

Year Award Winners
1987 
Dr R J A Wanders 
1988 
Prof R Matalon 
1989 
Dr K Hyland and Dr P T Clayton 
1990 
Dr N Gregersen et al 
1991 
Dr R J A Wanders and Dr J Heikoop 
1992 
Dr K L Chambliss and Dr C F Lee et al 
1993 
Dr E Mayatapek and Dr G F Hoffmann 
1994 
Dr R J A Wanders and Dr C W T van Roermund 
1995 
Prof J Jaeken et al and Dr M Spada et al 
1996 
Dr G A Jansen et al and Dr K H Carpenter et al 
1997 
Dr P Y Jensen et al and Dr R Santer et al 
1998 
Dr K Hyland et al and Dr P J Waters et al 
1999 
K Peltola et al and Dr S Munro et al 
2001 
Prof G Matthijs and Dr L Bonafe 
2002 
Dr G Parenti et al and Ms C B Pedersen et al 
2004 
Dr S Ferdinandusse et al and Dr P B Mills et al 
2005 
Dr P B Mills, Dr E Struys and Dr AArfi et al 
2007 
Dr H R Waterham and PD Dr T Marquardt 
2008 
Dr D Coelho and Prof M C Sa Miranda 
2010 
Dr D Lefeber 
2011 
Dr Navarro-Sastre et al and Dr C Fauth et al 
2012 
Dr K Tuschl et al and Dr D Martinelli et al 
2013 
Dr F Tort and Prof R Steinfeld 
2014 
Dr S Houten and Dr C Staufner 
2015 
Dr S Rahman and Dr Acquaviva-Bourdain 
2016 
Dr D Lefeber and Dr S B Wortmann 
2018 
Dr M Veiga-da-Cunha and Miss A Willems 
2019 
Dr P B Mills and Dr A Garcia-Cazorla 
2020 
Dr S Ferdinandusse and Dr A Pujol 

Symposium Travel Scholarship Application

OPENING DATE

Applications will be accepted between 02 Feb 2019 and 30-Mar-2019 (Midnight GMT)

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Errors of Metabolism (SSIEM)
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